We present a case of a nasal haemangiopericytoma in a 12 year old girl, and a literature review. The child presented with nasal obstruction without epistaxis, the . Objective: To describe one case of myopericytoma in nasal cavity. Sennes LU, Sanchez TG, Butugau O, Miniti A. Hemangiopericitoma nasal: relato de um. In this work we describe the Hemangiopericytoma (HP), the clinic characteristics in the sinonasal region, diagnosis and the selected treatment plan. Next, we.
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Bleeding is the most common symptom. In spite of being rare, the myopericytomas must be recalled in the differential diagnosis of the well delimited masses upon tomography. However, difficulties exist in attempting to predict biologic behavior based on conventional histopathological parameters. Medical College Uttarakhand, India. Brockbank analyzed a series of 35 cases in the oral cavity which included: The treatment of choice for HPC is wide surgical excision, with preceding ligation of the vascular bundle that nourishes the neoplastic tissue, thus achieving reduction of the size of the neoplasm as well as its removal.
Etiology is still not clarified, however, hypertension, past trauma, pregnancy and corticosteroid use can be causal factors, as described by Angouridakis et al. Sibilla Cintia Silva Dr. Basal lamina surrounds individual cells, tapered cytoplasmic extensions, orderly bundles of filaments.
Myopericytoma in Nasal Cavity
Here we report a case of rare nasal mass, which presented with nasal obstruction and epistaxis. Approved on April 11 Hemangiopericytoma of the head and neck. The treatment of choice is surgical resection.
This is an Open Access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. Hemangiopericytoma is a rare tumor type, first described in by Stout and Murray. The histopathological staining supported the diagnosis of HPC, this was further confirmed by immunohistochemistry IHC in which CD99 showed strong positivity.
Open in a separate window. The HPCs exhibit an unpredictable biologic behavior. Vascular markers stain only the endothelial cells of the blood vessels.
Following the surgery, the patient presented fast regrowth of the lesion, with partial response to chemotherapy and radiotherapy. A rare sinonasal tumor.
Staghorn vessels are prominent.
Hemangiopericitoma de cavidad nasal
It presents a characteristic cell proliferation now round, now spindle-shaped, without atypias, in bundles with syncytial arrangements. Svetlozar Haralanov Evelina Haralanova Dr. This website is intended for pathologists and laboratory personnel, who understand that medical information is imperfect and must be interpreted using reasonable medical judgment.
The negative staining with Hemangiopericitoa rules out synovial sarcoma. Use your account on the social network Facebook, to create a profile on BusinessPress. This type of controversy can only be solved by advanced diagnostic methods like immunohistochemistry and use of Vimentin, CD34, Smooth muscle actin and CD Hemangiopericytoma HPC is a soft tissue tumor arising from Zimmermann’s pericytes, which are modified smooth-muscle cells in the periphery of blood vessels.
A twelve-year-old male patient noted the presence of a firm painless right-side retroauricular lymph node of 1 cm in diameter, which at first remained unchanged for six months, but subsequently enlarged progressively.
Lilian Carmen Even Dr. Services on Demand Journal. On palpation, the lesion nsal sessile, the growth pattern was intermittent and the surface appeared smooth.
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The efficacy of radiation therapy is doubtful because HPC is considered to be radioresistant, but radiation therapy can be useful in the treatment of aggressive HPC and incomplete resections. Ayuda de la revista. However, the pericytes, in which they originate, possess characteristics of both smooth muscle and endothelial cells.
Recommended treatment is wide surgical resection.
Sinonasal hemangiopericytoma: A rare case report with review of literature
The surgical approach naxal a Weber-Ferguson incision lateral rhinotomy with upper lip splitting and extending to the lower eyelid with en bloc excision of the medial maxilla and the ethmoid labyrinth. Today hemangiopericiyoma important to carry out the selective tumoral embolization before all the techniques to make the surgical access easier. Deeper tissue cuts studied which revealed that mass could be hemangiopericytoma Fig. Spatola C, Privitera G.
Shortly afterwards, magnetic resonance imaging revealed that this lesion had undergone significant growth, while maintaining the same invasion pattern. Le neoplasie maligne non epiteliali delle V.
All the contents of this journal, except where otherwise noted, is licensed under a Creative Commons Attribution License. A tumour with perivascular myoid differentiation: The tumor cells are of variable small, ovoid to spindle shaped showing ill-defined cell boundaries.
Immunohistochemistry aids in differentiation and commonly shows diffuse expression of smooth muscle actin and focal expression of CD34 4 Overlying mucosa appeared normal in color. Final biopsy report of excised mass was sent to different pathologists at different hemangiopericitpma.
Correspondence Jomar Rezende Carvalho R.
Systematic review of treatment and prognosis of nasa, hemangiopericytoma. Accessed December 31st, In the described case, the complete resection of the tumor was possible because it included the open and the endoscopic approaches.
The tumor cells are round to ovoid in shape with well-defined cell boundaries. Hemangiopericytoma usually evolves with slow and non-painful growth that progresses towards nasal obstruction and epistaxis, which are the most common symptoms.